J.R., a 13-year-old with cystic fibrosis, is being seen in the outpatient clinic for a biannual evaluation. J.R. lives at home with his parents and 7-year-old sister, C.R., who also has cystic fibrosis. J.R. reports that he “doesn't feel good,” explaining that he has missed the last week of school, doesn't have any energy, is coughing more, and is having “a hard time breathing.
1. What additional data should be obtained from J.R. and his parents?
2. Describe the pathophysiology of cystic fibrosis (CF). Be sure to address the multisystem
component of this disorder